Pathways of ammonia detoxification to GLN in muscles connected with Increased usage with the BCAA and ?-KG (cataplerosis) and suggested effects of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Favourable outcome of BCAA on ammonia detoxification to GLN may be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylb